J Oral Med Oral Surg
Volume 25, Number 4, 2019
|Number of page(s)||4|
|Section||Cas clinique et revue de la littérature / Up-to date review and case report|
|Published online||12 September 2019|
Up-to Date Review And Case Report
Characteristics of the odontological management of patients with progressive ossifying fibrodyplasia
CHU Ibn Rochd, Centre de Consultation et Traitement dentaire, Service d'odontologie chirurgicale, Casablanca, Maroc
* Correspondence: email@example.com
Accepted: 15 June 2019
Introduction: Progressive ossifying fibrodysplasia (POF) is a rare autosomal dominant disease characterized by the congenital malformation of the big toes and progressive postnatal heterotopic ossification of soft tissues with characteristic anatomical profiles. The maxillofacial region may also be affected. Observation: A 24-year-old man was referred by a traumatologist for the restoration of the oral cavity. He showed characteristic signs of POF. Oral clinical examination showed limitation of the oral opening, multiple dental caries, dental necrosis, and an asymptomatic impacted 48. Management included motivation for oral hygiene, scaling and dental extractions, followed by a prescription of steroidal anti-inflammatory drugs at a single dose of 2 mg/kg/day for 4 days. Discussion: The management of patients with POF in oral surgery has particularities. Dental care must be performed in brief sessions. The patient must be in a semi-sitting position, with the neck held upright, to avoid hyper extension of the neck and to improve comfort and safety. A prescription for corticosteroids is necessary after dental care to prevent possible heterotopic ossification. Through this article, we highlight the characteristics of POF, therapeutic attitude, and precautions to take to avoid possible complications.
Key words: progressive ossifying fibrodysplasia / dental care / oral health
© The authors, 2019
This is an Open Access article distributed under the terms of the Creative Commons Attribution License (http://creativecommons.org/licenses/by/4.0), which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
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