J Oral Med Oral Surg
Volume 25, Number 3, 2019
|Number of page(s)||3|
|Section||Cas clinique et revue de la littérature / Up-to date review and case report|
|Published online||22 August 2019|
Up-to Date Review And Case Report
Progressive facial hemiatrophy (Parry-Romberg syndrome): short case report
Faculté d'odontologie, Université Claude Bernard Lyon I, 11 rue Guillaume Paradin, 69008 Lyon, France
2 Unité tête et cou, chirurgie oncologique, CRLCC Léon Bérard, 28 promenade Lea et Napoleon Bullukian, 69008 Lyon, France
* Corresponding author: firstname.lastname@example.org
Accepted: 29 June 2019
Introduction: The Parry Romberg syndrome (PRS) is a mosaic disease of unknown aetiology which mostly affects women. The facial hemiatrophy generally begins during the early childhood. It has a great impact on social life, and aesthetic rehabilitation is a major challenge. Observation: A 38 years-old-female patient presented with an enucleation of the left eye, due to multiple hamartomas and progressive facial hemiatrophy. The placement of 2 extraoral implants was proposed to bear an ocular epithesis. Comments: PRS develops between the 2nd and 20th year of life, and stabilizes at the adult age. Its main characteristic is a progressive facial hemiatrophy, which involves skin, fat tissues, muscles and osteocartilaginous tissues. 20% of patients have neurological symptoms, and epilepsy is often described as a side effect of the disease. Conclusion: Diagnosis of localized scleroderma has to be eliminated, as these 2 entities are very similar. Major facial reconstructive surgery is often proposed to restore aesthetics.
Key words: facial hemiatrophy / progressive / rehabilitation / follow up
© The authors, 2019
This is an Open Access article distributed under the terms of the Creative Commons Attribution License (http://creativecommons.org/licenses/by/4.0), which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
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