| Issue |
J Oral Med Oral Surg
Volume 26, Number 1, 2020
|
|
|---|---|---|
| Article Number | 5 | |
| Number of page(s) | 10 | |
| Section | Cas clinique et revue de la littérature / Up-to date review and case report | |
| DOI | https://doi.org/10.1051/mbcb/2019030 | |
| Published online | 07 January 2020 | |
Up-to Date Review And Case Report
Surgical-orthodontic treatment in patients with Ehlers–Danlos syndrome: a report of two familial cases
1
Unité de Pathologie-Chirurgie buccale, Pôle de Médecine et de Chirurgie bucco-dentaires, Hôpital Civil, Hôpitaux Universitaires de Strasbourg, Strasbourg, France
2
Pratique privée, Colmar, France
3
Université de Strasbourg, Faculté de Chirurgie Dentaire, Strasbourg, France
4
Unité d'Odontologie Pédiatrique, Pôle de Médecine et de Chirurgie bucco-dentaires, Hôpital Civil, Hôpitaux Universitaires de Strasbourg, Strasbourg, France
5
Centre de Référence des Manifestations Odontologiques des Maladies Rares, Pôle de Médecine et de Chirurgie bucco-dentaires, Hôpital Civil, Hôpitaux Universitaires de Strasbourg, Strasbourg, France
6
INSERM, UMR 1260, Regenerative Nanomedicine (RNM), FMTS, 11 rue Humann, Strasbourg 67000, France
* Correspondence: hchapuis.hc@gmail.com
Received:
27
August
2019
Accepted:
17
October
2019
Introduction: Ehlers–Danlos syndromes (EDS) are a group of rare inherited connective tissue disorders that affect the synthesis and structure of collagen in a ubiquitous manner. The clinical presentation can vary according to the associated genetic mutation. The 2017 international classification of EDS describes 13 types of EDS. Observation: The first part of this paper describes the surgical-orthodontic treatment for two sisters affected by a common and familial form of EDS, with a follow-up period of 8 years. The main symptoms were agenesis, impacted teeth, and delayed eruptions. Discussion: The second part proposes a review of oro-dental manifestations and discusses therapeutic approaches for patients with EDS. Conclusion: EDS can affect the oro-dental region with numerous consequences. Recognition of clinical symptoms and radiological signs is essential to provide appropriate dental care. Moreover, complete clinical and radiological assessment can allow early diagnosis of EDS.
Key words: Ehlers–Danlos / oral / dental / management
© The authors, 2020
This is an Open Access article distributed under the terms of the Creative Commons Attribution License (https://creativecommons.org/licenses/by/4.0), which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
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